Subacute necrotizing encephalopathy in an acidotic child.

نویسندگان

  • P G Procopis
  • B Turner
  • G Selby
چکیده

Subacute necrotizing encephalopathy was described originally by Leigh (1951). Further case reports reviewed by Ebels, Blokzijl, and Troelstra (1965) have confirmed this condition as a neuropathological entity but ideas concerning its aetiology have remained speculative. Recently Worsley, Brookfield, Elwood, Noble, and Taylor (1965) have reported a case, with confirmation at necropsy, in which there was a persistent lactic acidosis during life. A sibling had died of a similar illness. The authors postulated a disturbance of lactic acid metabolism in this disease. The present report describes a patient with infantile subacute necrotizing encephalopathy in whom a persistent acidosis was a feature of the illness during life.

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عنوان ژورنال:
  • Journal of neurology, neurosurgery, and psychiatry

دوره 30 4  شماره 

صفحات  -

تاریخ انتشار 1967